本病例報告介紹了一名在產前檢查中發現1.5 x 1.5 公分先天性臍部囊腫的新生兒。最初懷疑為臍腹壁疝氣，因此進行了全面檢查，未發現其他相關的異常。在進行手術切除後，病灶被確診為先天性尿道囊腫。嬰兒對手術耐受良好，於術後第7天順利出院，未出現併發症。此病例強調了在新生兒臍部囊腫中進行鑑別診斷的重要性，臍尿管囊腫可能有類似其他臍部異常的臨床表現如臍腹壁疝氣。早期診斷和及時手術可降低感染的病發症。本病例強調了臍尿管遺跡的多樣性表現，以及在處理臍部異常時提高臨床懷疑的重要性。

Introduction: The umbilicus is a common site of various embryological anom-alies. Congenital umbilical cord hernia involves the herniation of abdominal con-tents into the umbilical cord, a condition often misdiagnosed as omphalocele. Case Presentation: We describe a rare case of a term male neonate with a prenatal diag-nosis of an umbilical cyst. Postnatally, the cyst ruptured, revealing exposed viscera with a blood-tinged discharge. Initial suspicion of congenital umbilical cord hernia led to imaging studies, which ruled out other gastrointestinal or genitourinary anomalies. Surgical exploration confirmed a urachal cyst, which was excised without complications. The patient had an uneventful recovery and was discharged in good condition. Discussion: Urachal cysts, though uncommon, can mimic other umbilical anomalies and may present atypically, as seen in our case. Early diagnosis and prompt surgical intervention are essential to prevent complications. This case em-phasizes the diverse presentations of urachal remnants and the importance of clinical suspicion in managing umbilical anomalies. Conclusion: Urachal cysts can present as umbilical cord hernias, complicating diagnosis. A thorough clinical evaluation, imaging, and surgical management are critical to ensuring favorable outcomes.