Proteus syndrome: Unveiling the anesthetic myths

We are presenting a nine year old male patient weighing 23 kg, diagnosed case of Proteus syndrome (PS) who was posted for closed reduction and internal fixation following fracture of left shaft of femur. He had a history of trauma of left leg one week before. Airway assessment showed Mallampati grade 4, tongue hemangioma and misaligned teeth. Systemic examination revealed multiple hemangiomas and asymmetric enlargement of both upper and lower limbs. All laboratory investigations were within normal limits.